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Table 4 Variables related to 21-hydroxylase deficiency according to phenotype

From: Cardiovascular risk in Cuban adolescents and young adults with congenital adrenal hyperplasia

 

Phenotype

p- value

SW

n = 8

SV

n = 5

NC

n = 9

Age at diagnosis

(years)

0.01 (0.01–1)

1 (0.01–8)

12 (6–18)

 < 0.01

Time since diagnosis (years)

14 (10–31)

11 (10–25)

8 (0.8–12)

 < 0.01

Hydrocortisone equivalent dose

mg/d

37.5 (15–40)

27.5 (15–50)

15 (15–17.5)

0.10

Hydrocortisone equivalent dose (mg/m2/d)

20 (12.9–27.1)

17.8 (7.5–31.4)

8.7 (8.7–10.6)

0.07

Testosterone (nmol/L)

2.9 (0.5–6.4) F

4.0 M

4.2 (1.1–9.2) F

7.0 (0.8–13.1) M

2.9 (0.5–6.4) F

4.0 M

0.91

17OHP (ng/mL)

12.4 (3.1–14)

13 (1.5–13.2)

2.4 (0.3–13)

0.03

CIMT (mm)

0.46 (0.4–0.55)

0.41(0.3–0.5)

0.52 (0.45–0.6)a

0.05

FMD

(%)

9.65 (0.0–17.96)

11.55 (4.29–19.47)

10.91 (2.61–19.85)a

0.84

Epicardial fat

(mm)

1.44 (0.0–5.8)

0.62 (0.0–1.1)

1.14 (0.0–5.0)

0.82

  1. SW Salt-wasting, SV simple virilizing, NC non-classic form, 170HP 17-hydroxyprogesterone, CIMT Carotid intima media thickness, FMD flow-mediated dilation
  2. an = 8. F female, M male