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Table 2 The summary of the reported cases of pheochromocytoma in patient with Turner syndrome

From: Pheochromocytoma as a rare cause of hypertension in a 46 X, i(X)(q10) turner syndrome: a case report and literature review

Authors, year of publication (reference)

Age

Karyotype

Size of pheochromocytoma

Clinical manifestations

Cardiovascular outcomes

Knisely et al. (1988) [11]

27

45,XO

7.5 cm

Hemorrhagic cerebral infarct

Sudden death

Landin-Wilhelmsen et al. (2004) [12]

39

45,X[46]/46,X + mar [4]

3.0 cm

Chest pain hypertension

Aortic dissection

Fatma et al. (2016) [13]

48

46 X,i(Xq)/45X

6.0 cm

Adrenal incidentaloma hypertension

Curative hypertension

In our case

21

46 X, i(X)(q10)

1.9 cm

Hypertension

Curative hypertension